Congenital contractural arachnodactyly (CCA) is an inherited disorder of connective tissue. The most characteristic features are arachnodactyly, multiple congenital contractures, dolichostenomelia, deformed external ears, kyphoscoliosis and camptodactyly. We report a case of CCA diagnosed at birth.
Journal Information
Vol. 71. Issue 06.
Pages 337-340 (November - December 1995)
Vol. 71. Issue 06.
Pages 337-340 (November - December 1995)
DOI: 10.2223/JPED.802
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Síndrome de Beals-Hecht: relato de um caso neonatal
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